(3S,4S,5S,6S)-6-(3-((2,4-di-tert-butyl-5-hydroxyphenyl)carbamoyl)-4-oxoquinolin-1(4H)-yl)-3,4,5-trihydroxytetrahydro-2H-pyran-2-carboxylicacid-D19;N-[2,4-Bis[1,1-di(methyl)ethyl]-5-hydroxyphenyl]-1,4-dihydro-4-oxo-3-quinolinecarboxamide-d19; Ivacaftor-d19; Kalydeco-d19;Ivacaftor-d19